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Article in English | IMSEAR | ID: sea-139786

ABSTRACT

Hutchinson Gilford Progeria Syndrome (HGPS) is a rare, sporadic, autosomal dominant syndrome that involves premature ageing and death at early age due to myocardial infarction or stroke. A 30-year-old male with clinical and radiologic features highly suggestive of HGPS is presented here with description of differential diagnosis, dental considerations and review of literature.


Subject(s)
Adult , Anodontia/diagnosis , Cranial Sutures/abnormalities , Craniofacial Abnormalities/diagnosis , Diagnosis, Differential , Frontal Bone/abnormalities , Humans , Male , Mandible/abnormalities , Mandibular Condyle/abnormalities , Nose/abnormalities , Parietal Bone/abnormalities , Progeria/diagnosis
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